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Generalised pustular psoriasis

Essential points for quick revision.

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Acute pustular systemic crisis

Waves of widespread sterile pustules with painful inflammation, fever, tachycardia or malaise can cause fluid and protein loss, electrolyte disturbance, sepsis, respiratory failure, high-output cardiac failure and shock.

Action: Arrange same-day admission and urgent dermatology review, assess ABCDE and extent, culture before but never instead of treating suspected infection, monitor organ function and calcium, provide temperature, fluid, nutritional and skin support, and start specialist flare therapy without systemic corticosteroid withdrawal.

Synopsis

Recognise a generalised pustular psoriasis flare as a potentially fatal neutrophilic emergency, exclude infection and drug pustulosis, stabilise systemic complications, and apply current specialist systemic and spesolimab criteria safely.

  • Generalised pustular psoriasis causes widespread visible or superficial non-follicular pustules on inflamed skin with systemic illness; pustules are sterile unless secondary infection complicates them.
  • Pustules may be conspicuous cream-yellow in any skin tone, while background erythema can look red, violaceous, grey-brown or dusky and is assessed with warmth, tenderness and swelling.
  • Ask about established plaque or pustular psoriasis, previous flares, pregnancy, infection, hypocalcaemia, medicine exposure and abrupt withdrawal of systemic corticosteroid or other psoriasis treatment.

Key red flags

Hypotension, hypoxia, confusion, oliguria, rapidly spreading painful pustulation, hypothermia or high fever, severe oedema, tetany, mucosal involvement, pregnancy, childhood, frailty, neutropenia, suspected sepsis or respiratory symptoms requires critical-care-level reassessment and urgent specialist treatment.

Organ-threatening flare

Hypotension, hypoxia, confusion, oliguria, marked calcium disturbance, tetany, extensive erosion or rapidly escalating oxygen and fluid need indicates critical illness.

Investigation priorities

01
Full blood count and differentialFirst step

Quantify neutrophilic inflammation and identify eosinophilia, cytopenia or infection risk.

Management branches

First-line emergency careAdmit, stabilise and sample

Widespread pustulation is accompanied by systemic symptoms, rapid progression or diagnostic uncertainty.

  1. Assess ABCDE, core temperature, haemodynamics, oxygen need, mental state, pain, extent, mucosae and urine output and involve dermatology immediately.
  2. Obtain full blood count, renal, liver, albumin, calcium, magnesium, CRP and appropriate cultures, biopsy a fresh lesion and document the complete medicine timeline.

Key medicines

Intravenous spesolimabGive 900 mg as a single intravenous infusion over 90 minutes; if flare symptoms persist, one additional 900 mg dose may be given 1 week later.
CiclosporinFor adult severe psoriasis, use 2.5 mg/kg/day orally in two divided doses, increasing gradually if needed to no more than 5 mg/kg/day under specialist supervision.
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Sources and review status5 sources · checked 27 Aug 2026 · clinical review pending
Sources

Sources and review status

National guidance is shown before implementation-dependent detail. Typical adult dose examples remain subject to patient factors, contraindications and the live BNF or specialist protocol. Source check completed 27 Aug 2026; clinical approval remains outstanding.

Authoring stateRapid draftClinical stateAwaiting reviewJurisdictionUnited Kingdom