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Livedo reticularis and thrombotic skin disease

Essential points for quick revision.

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Acute ischaemia or thrombotic systemic disease

A sudden cold painful limb or digit, absent pulses, sensory or motor loss, rapidly advancing angular necrosis, shock, neurological deficit, renal decline after vascular instrumentation or disseminated purpura can indicate arterial occlusion, embolism, DIC, TTP, calciphylaxis or severe infection.

Action: Arrange immediate vascular or emergency admission, assess ABCDE and limb viability, obtain blood and imaging without delaying revascularisation or sepsis care, and involve haematology, renal, neurology or dermatology according to the systemic phenotype.

Synopsis

Distinguish reversible livedo reticularis from pathological livedo racemosa and retiform infarction, assess perfusion and thrombotic drivers, select deep tissue appropriately, and escalate ischaemia without empirical anticoagulation.

  • Physiological livedo reticularis is a regular closed purple network provoked by cold, usually symmetrical on limbs and substantially resolving with warming.
  • Livedo racemosa is persistent, irregular, broken and often wider-meshed across limbs, buttocks or trunk; it raises antiphospholipid syndrome, Sneddon syndrome and other systemic vasculopathies.
  • Retiform purpura is fixed non-blanching angular or branching ischaemia that progresses towards ulcer or necrosis and indicates occluded or destroyed vessels rather than benign vasospasm.

Key red flags

Rest pain, tissue coldness, absent pulses, fixed retiform purpura, necrosis, new focal neurology, severe headache, renal injury, fever, shock, thrombocytopenia, pregnancy morbidity with thrombosis or a rapidly ulcerating livedoid pattern requires urgent specialist review.

Retiform infarction

Fixed angulated non-blanching patches become painful, blistered or black as branching vascular territories lose flow.

Investigation priorities

01
Warmth and full vascular examinationFirst step

Separate functional vasospasm from fixed ischaemia and identify limb-threatening disease immediately.

Management branches

First-line pattern sequenceWarm, map and test perfusion

A net-like purple, grey or brown skin pattern is newly noticed.

  1. Photograph the distribution with consent before and after safe warming and determine whether the network is regular and closed or broken, fixed and widespread.
  2. Ask about pain, ulcer, thrombosis, pregnancy morbidity, vascular procedures, kidney disease, fever and neurological symptoms and examine pulses, refill, temperature and sensation.
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Sources and review status4 sources · checked 27 Aug 2026 · clinical review pending
Sources

Sources and review status

National guidance is shown before implementation-dependent detail. Typical adult dose examples remain subject to patient factors, contraindications and the live BNF or specialist protocol. Source check completed 27 Aug 2026; clinical approval remains outstanding.

Authoring stateRapid draftClinical stateAwaiting reviewJurisdictionUnited Kingdom